Zimmerman-Tumor, a Phakomatous Choristoma of the Eyelid
Ober S., Schmitz A., Langefeld S., Hinkeldey O., Press U. P.
Augenklinik des Brüderkrankenhauses, Trier
Purpose: We report a case of a rare phakomatous choristoma of the left medial lower lid and anterior orbit, that was excised through a transconjunctival incision.
Method: This case occurred in an 9-month old infant that was refered to us with the estimated diagnosis of a dermoid cyst for surgical treatment. Sonographic examination showed a 15x10x6mm circumscribet solid and rare vascularized tumor. The tumor was excised through a transconjunctival approach, followed by a histopathological work-up.
Results: Due to the histopathological work-up the diagnosis phakomatous choristoma was set. The surgical procedure and the histopathological work-up are presented.
Conclusions: The phakomatous choristoma, also described as Zimmerman-tumor, is a rare tumor of the lid and the anterior orbit in infants. It is assumed that the cells of the phakomatous choristoma are from lenticular origin.
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